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Title: Defective (U-14 C) palmitic acid oxidation in Duchenne muscular dystrophy

Journal Article · · Neurology; (United States)
DOI:https://doi.org/10.1212/WNL.35.1.96· OSTI ID:5777403

Compared with normal skeletal muscle, muscle from patients with Duchenne dystrophy had decreased (U-14 C) palmitic acid oxidation. (1-14 C) palmitic acid oxidation was normal. These results may indicate a defect in intramitochondrial fatty acid oxidation.

Research Organization:
Washington Univ. School of Medicine, St. Louis, MO
OSTI ID:
5777403
Journal Information:
Neurology; (United States), Vol. 35:1
Country of Publication:
United States
Language:
English