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Germline mosaicism at the fragile X locus

Journal Article · · American Journal of Medical Genetics
; ;  [1]
  1. Ohio State Univ., Columbus, OH (United States); and others

We have identified a fragile X syndrome pedigree where the disorder is associated with a molecular deletion. The deletion was present in the DNA of 2 sons but was absent in the mother`s somatic cell (lymphocyte) DNA. The results are consistent with the deletion arising as a postzygotic event in the mother, who therefore is germinally mosaic. This finding has important implications for counseling fragile X families with deletion mutations. 13 refs., 2 figs.

Sponsoring Organization:
USDOE
OSTI ID:
91131
Journal Information:
American Journal of Medical Genetics, Journal Name: American Journal of Medical Genetics Journal Issue: 3 Vol. 55; ISSN 0148-7299; ISSN AJMGDA
Country of Publication:
United States
Language:
English

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