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Primary amyloid heart disease presenting as hypertrophic obstructive cardiomyopathy

Journal Article · · Cathet. Cardiovasc. Diagn.; (United States)
OSTI ID:5094111
This report describes the unusual presentation of a patient with primary cardiac amyloidosis. Initial clinical symptoms and hemodynamic studies, including Technetium-99m-pyrophosphate scintigraphy, suggested hypertrophic obstructive cardiomyopathy, but endomyocardial biopsy revealed diffuse amyloid infiltration. Only two other cases of left ventricular outflow tract obstruction due to cardiac amyloidosis have been reported. The false-negative technetium-99m-pyrophosphate scintigram in this patient argues for the use of endomyocardial biopsy to aid in the diagnosis of left ventricular hypertrophy.
Research Organization:
Walter Reed Army Medical Center, Washington, DC
OSTI ID:
5094111
Journal Information:
Cathet. Cardiovasc. Diagn.; (United States), Journal Name: Cathet. Cardiovasc. Diagn.; (United States) Vol. 3; ISSN CCDID
Country of Publication:
United States
Language:
English