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Title: Crouzon’s Syndrome with Life-Threatening Ear Bleed: Ruptured Jugular Vein Diverticulum Treated by Endovascular Embolization

Abstract

Crouzon’s syndrome is the commonest variety of syndromic craniosynostosis. Life-threatening ear bleed due to ruptured jugular venous diverticulum in Crouzon’s syndrome has not been described previously. In patients with syndromic craniosynostosis, definitive repair of jugular diverticulum by open surgery is fraught with high risk of bleeding, poor functional outcomes, and even death. A 24-year-old woman with Crouzon’s syndrome presented with conductive hearing loss and recurrent episodes of torrential bleeding from her left ear. On computed tomography, a defect in the roof of jugular fossa containing jugular venous diverticulum immediately inferior to the bony external auditory canal was seen. The clinical presentation, imaging features, and endovascular management of Crouzon’s syndrome due to a ruptured jugular venous diverticulum is described.

Authors:
; ;  [1]
  1. Lilavati Hospital and Research Centre, Department of Interventional Neuroradiology (India)
Publication Date:
OSTI Identifier:
22469847
Resource Type:
Journal Article
Journal Name:
Cardiovascular and Interventional Radiology
Additional Journal Information:
Journal Volume: 38; Journal Issue: 4; Other Information: Copyright (c) 2015 Springer Science+Business Media New York and the Cardiovascular and Interventional Radiological Society of Europe (CIRSE); http://www.springer-ny.com; Country of input: International Atomic Energy Agency (IAEA); Journal ID: ISSN 0174-1551
Country of Publication:
United States
Language:
English
Subject:
62 RADIOLOGY AND NUCLEAR MEDICINE; AUDITORY ORGANS; BIOMEDICAL RADIOGRAPHY; COMPUTERIZED TOMOGRAPHY; DEATH; HEALTH HAZARDS; PATIENTS; RUPTURES; SURGERY; VASCULAR DISEASES; VEINS; WOMEN

Citation Formats

Mondel, Prabath Kumar, E-mail: prabathmondel@gmail.com, Anand, Sunanda, E-mail: sunandaanand@gmail.com, and Limaye, Uday S., E-mail: uslkem@gmail.com. Crouzon’s Syndrome with Life-Threatening Ear Bleed: Ruptured Jugular Vein Diverticulum Treated by Endovascular Embolization. United States: N. p., 2015. Web. doi:10.1007/S00270-014-0983-1.
Mondel, Prabath Kumar, E-mail: prabathmondel@gmail.com, Anand, Sunanda, E-mail: sunandaanand@gmail.com, & Limaye, Uday S., E-mail: uslkem@gmail.com. Crouzon’s Syndrome with Life-Threatening Ear Bleed: Ruptured Jugular Vein Diverticulum Treated by Endovascular Embolization. United States. doi:10.1007/S00270-014-0983-1.
Mondel, Prabath Kumar, E-mail: prabathmondel@gmail.com, Anand, Sunanda, E-mail: sunandaanand@gmail.com, and Limaye, Uday S., E-mail: uslkem@gmail.com. Sat . "Crouzon’s Syndrome with Life-Threatening Ear Bleed: Ruptured Jugular Vein Diverticulum Treated by Endovascular Embolization". United States. doi:10.1007/S00270-014-0983-1.
@article{osti_22469847,
title = {Crouzon’s Syndrome with Life-Threatening Ear Bleed: Ruptured Jugular Vein Diverticulum Treated by Endovascular Embolization},
author = {Mondel, Prabath Kumar, E-mail: prabathmondel@gmail.com and Anand, Sunanda, E-mail: sunandaanand@gmail.com and Limaye, Uday S., E-mail: uslkem@gmail.com},
abstractNote = {Crouzon’s syndrome is the commonest variety of syndromic craniosynostosis. Life-threatening ear bleed due to ruptured jugular venous diverticulum in Crouzon’s syndrome has not been described previously. In patients with syndromic craniosynostosis, definitive repair of jugular diverticulum by open surgery is fraught with high risk of bleeding, poor functional outcomes, and even death. A 24-year-old woman with Crouzon’s syndrome presented with conductive hearing loss and recurrent episodes of torrential bleeding from her left ear. On computed tomography, a defect in the roof of jugular fossa containing jugular venous diverticulum immediately inferior to the bony external auditory canal was seen. The clinical presentation, imaging features, and endovascular management of Crouzon’s syndrome due to a ruptured jugular venous diverticulum is described.},
doi = {10.1007/S00270-014-0983-1},
journal = {Cardiovascular and Interventional Radiology},
issn = {0174-1551},
number = 4,
volume = 38,
place = {United States},
year = {2015},
month = {8}
}