Angiography of Hepatic Vascular Malformations Associated with Hereditary Hemorrhagic Telangiectasia

Journal Article · Tue Apr 15 00:00:00 EDT 2003 · Cardiovascular and Interventional Radiology

DOI:https://doi.org/10.1007/S00270-002-1507-Y· OSTI ID:21088414

Hashimoto, Manabu; Tate, Etuko; Nishii, Toshiaki; Watarai, Jiro ^[1]; Shioya, Takanobu ^[2]; White, Robert I ^[3]

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1. Akita University School of Medicine, 1-1-1 Hondo, Akita City, Akita 010-8543, Department of Radiology (Japan)
2. Akita University School of Medicine, 1-1-1 Hondo, Akita City, Akita 010-8543, Department of Internal Medicine (Japan)
3. Yale University School of Medicine, New Haven, Connecticut, Department of Diagnostic Radiology (United States)

Purpose: To describe the angiographic features of hepatic involvement in hereditary hemorrhagictelangiectasia (HHT), particularly the presence of portovenous shunts. Methods: We reviewed the angiographic findings of seven patients with HHT. The patients comprised three women and four men with a mean age of 51 years. Results: Intrahepatictelangiectasias were found in all seven patients and shunts between three vascular channels were found in six of seven patients. In the four patients who had portovenous shunts combined with arterioportal shunts, the portovenous shunts were large. Three patients had noportovenous shunts. Two of these patients had arteriovenous shunts, and one had no shunt. The mean age (69 years) of the patients with portovenous shunts was older than those without portovenous shunts (26 years). Conclusions: Hepatic vascular lesions in HHT are varied, ranging from telangiectasias to large shunts between three vascular channels. In an advanced stage of involvement, large portovenous shunts are present.

• OSTI ID: 21088414
• Journal Information: Cardiovascular and Interventional Radiology, Vol. 26, Issue 2; Other Information: DOI: 10.1007/s00270-002-1507-Y; Copyright (c) 2003 Springer-Verlag New York, Inc.; www.springer-ny.com; Country of input: International Atomic Energy Agency (IAEA); ISSN 0174-1551
• Country of Publication: United States
• Language: English

Related Subjects

62 RADIOLOGY AND NUCLEAR MEDICINE
BIOMEDICAL RADIOGRAPHY
BLOOD VESSELS
BYPASSES
LIVER
MALFORMATIONS
PATIENTS
WOMEN